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Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis

Received: 3 August 2020     Accepted: 13 August 2020     Published: 19 August 2020
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Abstract

Background: Progressive familiar intrahepatic cholestasis (PFIC) is a group of rare cholestatic liver diseases whose main features are itching, jaundice and even liver failure. Many studies have been reported in clinical reports, but the care of PFIC is rarely described. Purpose: To provide a summary and recommendations for the setup of strategies for PFIC patient care. Material and methods: A non-systematic review of PFIC nursing research until July 12, 2020. Use online search engines (PubMed, Medline, Embase, Web of Science, and CINAHL) to find PFIC nursing-related content, sort and summarize nursing-related content. Results: As a rare disease, there is limited research in PFIC nursing. The main care measures of PFIC including nursing interventions and evaluation tools. Nursing intervention is divided into general symptom care and nursing care of postoperative complications. Evaluation tools mainly focus on quality of life assessment and evaluation of itching. Conclusions: Nurses should pay attention to the use of scales when caring for PFIC patients, and observe whether specific nursing measures can help improve patients’ quality of life. PFIC nursing interventions and evaluation tools should be tailored according to PFIC clinical manifestation. A multidisciplinary collaborative approach is encouraged for proper management and tailoring therapy according to clinical manifestation.

Published in American Journal of Nursing Science (Volume 9, Issue 5)
DOI 10.11648/j.ajns.20200905.11
Page(s) 310-315
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2020. Published by Science Publishing Group

Keywords

Progressive Familial Intrahepatic Cholestasis (PFIC), Nursing, Evaluation, Itching, Quality of Life, Intervention

References
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Cite This Article
  • APA Style

    Ni Zhang, Yuanzong Song, Meixue Chen, Lingli Cai, Manli Liu, et al. (2020). Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis. American Journal of Nursing Science, 9(5), 310-315. https://doi.org/10.11648/j.ajns.20200905.11

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    ACS Style

    Ni Zhang; Yuanzong Song; Meixue Chen; Lingli Cai; Manli Liu, et al. Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis. Am. J. Nurs. Sci. 2020, 9(5), 310-315. doi: 10.11648/j.ajns.20200905.11

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    AMA Style

    Ni Zhang, Yuanzong Song, Meixue Chen, Lingli Cai, Manli Liu, et al. Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis. Am J Nurs Sci. 2020;9(5):310-315. doi: 10.11648/j.ajns.20200905.11

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  • @article{10.11648/j.ajns.20200905.11,
      author = {Ni Zhang and Yuanzong Song and Meixue Chen and Lingli Cai and Manli Liu and Weiwei Wang and Qingran Lin},
      title = {Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis},
      journal = {American Journal of Nursing Science},
      volume = {9},
      number = {5},
      pages = {310-315},
      doi = {10.11648/j.ajns.20200905.11},
      url = {https://doi.org/10.11648/j.ajns.20200905.11},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajns.20200905.11},
      abstract = {Background: Progressive familiar intrahepatic cholestasis (PFIC) is a group of rare cholestatic liver diseases whose main features are itching, jaundice and even liver failure. Many studies have been reported in clinical reports, but the care of PFIC is rarely described. Purpose: To provide a summary and recommendations for the setup of strategies for PFIC patient care. Material and methods: A non-systematic review of PFIC nursing research until July 12, 2020. Use online search engines (PubMed, Medline, Embase, Web of Science, and CINAHL) to find PFIC nursing-related content, sort and summarize nursing-related content. Results: As a rare disease, there is limited research in PFIC nursing. The main care measures of PFIC including nursing interventions and evaluation tools. Nursing intervention is divided into general symptom care and nursing care of postoperative complications. Evaluation tools mainly focus on quality of life assessment and evaluation of itching. Conclusions: Nurses should pay attention to the use of scales when caring for PFIC patients, and observe whether specific nursing measures can help improve patients’ quality of life. PFIC nursing interventions and evaluation tools should be tailored according to PFIC clinical manifestation. A multidisciplinary collaborative approach is encouraged for proper management and tailoring therapy according to clinical manifestation.},
     year = {2020}
    }
    

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    T1  - Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis
    AU  - Ni Zhang
    AU  - Yuanzong Song
    AU  - Meixue Chen
    AU  - Lingli Cai
    AU  - Manli Liu
    AU  - Weiwei Wang
    AU  - Qingran Lin
    Y1  - 2020/08/19
    PY  - 2020
    N1  - https://doi.org/10.11648/j.ajns.20200905.11
    DO  - 10.11648/j.ajns.20200905.11
    T2  - American Journal of Nursing Science
    JF  - American Journal of Nursing Science
    JO  - American Journal of Nursing Science
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    EP  - 315
    PB  - Science Publishing Group
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    UR  - https://doi.org/10.11648/j.ajns.20200905.11
    AB  - Background: Progressive familiar intrahepatic cholestasis (PFIC) is a group of rare cholestatic liver diseases whose main features are itching, jaundice and even liver failure. Many studies have been reported in clinical reports, but the care of PFIC is rarely described. Purpose: To provide a summary and recommendations for the setup of strategies for PFIC patient care. Material and methods: A non-systematic review of PFIC nursing research until July 12, 2020. Use online search engines (PubMed, Medline, Embase, Web of Science, and CINAHL) to find PFIC nursing-related content, sort and summarize nursing-related content. Results: As a rare disease, there is limited research in PFIC nursing. The main care measures of PFIC including nursing interventions and evaluation tools. Nursing intervention is divided into general symptom care and nursing care of postoperative complications. Evaluation tools mainly focus on quality of life assessment and evaluation of itching. Conclusions: Nurses should pay attention to the use of scales when caring for PFIC patients, and observe whether specific nursing measures can help improve patients’ quality of life. PFIC nursing interventions and evaluation tools should be tailored according to PFIC clinical manifestation. A multidisciplinary collaborative approach is encouraged for proper management and tailoring therapy according to clinical manifestation.
    VL  - 9
    IS  - 5
    ER  - 

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Author Information
  • College of Nursing, Jinan University, Guangzhou, China

  • Department of Neonatal, The First Affiliated Hospital of Jinan University, Guangzhou, China

  • College of Nursing, Jinan University, Guangzhou, China

  • College of Nursing, Jinan University, Guangzhou, China

  • College of Nursing, Jinan University, Guangzhou, China

  • College of Nursing, Jinan University, Guangzhou, China

  • Department of Nursing, The First Affiliated Hospital of Jinan University, Guangzhou, China

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