Case Report
Amniotic Band Syndrome with Supernumerary Nostril: A Case Report
Issue:
Volume 11, Issue 1, June 2025
Pages:
1-4
Received:
27 April 2025
Accepted:
8 May 2025
Published:
18 June 2025
Abstract: Amniotic band syndrome is a rare congenital disorder resulting from the entrapment of fetal parts, particularly limbs or digits, in fibrous amniotic bands during intrauterine development. This condition is characterized by a wide spectrum of anomalies affecting multiple systems. Its estimated birth prevalence ranges from 1 in 1,200 to 1 in 15,000 live births. Supernumerary nostril—also referred to as triple or accessory nostril—is another rare congenital anomaly involving the presence of an additional nostril, which may or may not be associated with accessory cartilage. Typically unilateral and isolated, supernumerary nostrils can, in some cases, coexist with other congenital malformations. However, the co-occurrence of supernumerary nostril and ABS has not been documented in the literature to date. In this report, we present a rare case of a female patient born with a supernumerary nostril located above the left nostril in the context of amniotic band syndrome. This appears to be the first documented case of such an association. The aim of this report is to highlight the unusual combination of these two distinct congenital conditions and to contribute to the body of knowledge on the phenotypic variability of ABS. This case underscores the importance of thorough clinical evaluation in patients with congenital anomalies and suggests that rare associations may exist between seemingly unrelated malformations. Further research is needed to explore potential embryological links and to determine whether this association is incidental or part of a broader, yet unidentified, syndrome.
Abstract: Amniotic band syndrome is a rare congenital disorder resulting from the entrapment of fetal parts, particularly limbs or digits, in fibrous amniotic bands during intrauterine development. This condition is characterized by a wide spectrum of anomalies affecting multiple systems. Its estimated birth prevalence ranges from 1 in 1,200 to 1 in 15,000 l...
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Research Article
The Place of Ct Scan in the Diagnosis of Frontal Mucoceles: A Report on Two Clinical Cases
Abdoul Wahab Haidara*
,
Hamidou Tounkara,
David Dackouo,
Aminata Fofana,
Harouna Sanogo,
Ali Dembelé,
Boubacar Dramé,
Bagouma Traoré,
Mariam Sangare,
Mahamadou Doumbia,
Oumou Coulibaly,
Demba Coulibaly,
Boubacar Sanogo,
Aniessa Kodio,
Djibril Samake,
Youssouf Sidibé,
Sidiki Dao,
Fatogoma Issa Kone
,
Boubacary Guindo,
Siaka Soumaoro,
Kadiatou Singare,
Mohamed Amadou Keita
Issue:
Volume 11, Issue 1, June 2025
Pages:
5-8
Received:
4 June 2025
Accepted:
16 June 2025
Published:
7 July 2025
DOI:
10.11648/j.ijo.20251101.12
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Abstract: Introduction: Paranasal sinus mucoceles are benign and expansive lesions, related to the accumulation of mucus in an obstructed sinus cavity. The frontal mucocele is the most common, representing 60 to 89% of cases. Despite their benign nature, these lesions can lead to serious complications by extension to orbital or intracranial structures. Clinically, they can manifest as frontal swelling, orbital pain, exophthalmos or visual disturbances, making diagnosis difficult in the early stages. Computed tomography (CT) plays a central role in visualizing the lesion, assessing its extension and guiding management. In a resource-limited setting like Mali, its access remains crucial. This work illustrates the importance of CT through two clinical cases managed at Nianankoro Hospital Fomba of Segou. Methodology: This is a retrospective study of two patients treated between January 2023 and January 2025. Clinical, radiological (CT) and surgical data were analyzed. The diagnosis was based on the identification of expansive hypodense lesions of the frontal sinus with bone erosion. Both patients underwent endonasal surgery. Clinical observations: The first patient, 45 years old, presented with a left frontal swelling that had been evolving for 10 years. CT scan revealed a frontal mucocele with bone lysis and early intracranial extension. Endonasal surgery resulted in a favorable outcome without recurrence. The second patient, 35 years old, followed for chronic frontal sinusitis, presented with right exophthalmos. CT scan showed a mucocele compressive fronto -ethmoidal without bone rupture. The surgical intervention resulted in regression of the signs. Conclusion: These cases illustrate the clinical diversity of frontal mucoceles and confirm the diagnostic value of CT, essential for early and effective management.
Abstract: Introduction: Paranasal sinus mucoceles are benign and expansive lesions, related to the accumulation of mucus in an obstructed sinus cavity. The frontal mucocele is the most common, representing 60 to 89% of cases. Despite their benign nature, these lesions can lead to serious complications by extension to orbital or intracranial structures. Clini...
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