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Fibrodysplasia Ossificans Progressiva: A Review with Presentation of a Case with Temporomandibular Extra-Articular Ankylosis

Received: 31 January 2018    Accepted: 16 February 2018    Published: 19 March 2018
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Abstract

Fibrodysplasia Ossificans Progressiva (FOP) is a connective tissue disorder that progressively affects tendons, ligaments, aponeurosis, fasciae and muscles which undergo fibrous cell proliferation that progresses to mature bone. It has a prevalence of 1 case per 2 million habitants, having reported less than 1000 cases worldwide. In the maxillofacial region, it might originate extra-articular temporomandibular ankylosis by ossification of ligaments, muscles of the mastication, head and a neck muscles; the most commonly affected are the masseters and sternocleidomastoids. The purpose of this article is to review the Fibrodysplasia Ossificans Progressiva (FOP) and to present the case of a 12-year-old male patient with FOP that causes extra-articular temporomandibular ankylosis. There is no effective proven treatment or prevention and the life expectancy of these patients approaches the 40 years of age, so the management of patients with FOP must be performed with a multidisciplinary approach in which the various health professionals work in a coordinated and joint way to offer a better quality of life to these patients and thus better understand the progression of the disease.

Published in International Journal of Clinical Oral and Maxillofacial Surgery (Volume 4, Issue 1)
DOI 10.11648/j.ijcoms.20180401.12
Page(s) 4-10
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Fibrodysplasia Ossificans Progressiva, Myositis Ossificans Systemic, Munchmeyer's Disease, Extra-Articular Temporomandibular Ankylosis, Ankylosis of the Temporomandibular Joint

References
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Cite This Article
  • APA Style

    Cárcamo Idiáquez Osmar Adán, Cortes Flores Michelle, Anchecta Castro Diana Marielos, Vivanco Pérez Israel, Navarro Zarate Adolfo. (2018). Fibrodysplasia Ossificans Progressiva: A Review with Presentation of a Case with Temporomandibular Extra-Articular Ankylosis. International Journal of Clinical Oral and Maxillofacial Surgery, 4(1), 4-10. https://doi.org/10.11648/j.ijcoms.20180401.12

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    ACS Style

    Cárcamo Idiáquez Osmar Adán; Cortes Flores Michelle; Anchecta Castro Diana Marielos; Vivanco Pérez Israel; Navarro Zarate Adolfo. Fibrodysplasia Ossificans Progressiva: A Review with Presentation of a Case with Temporomandibular Extra-Articular Ankylosis. Int. J. Clin. Oral Maxillofac. Surg. 2018, 4(1), 4-10. doi: 10.11648/j.ijcoms.20180401.12

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    AMA Style

    Cárcamo Idiáquez Osmar Adán, Cortes Flores Michelle, Anchecta Castro Diana Marielos, Vivanco Pérez Israel, Navarro Zarate Adolfo. Fibrodysplasia Ossificans Progressiva: A Review with Presentation of a Case with Temporomandibular Extra-Articular Ankylosis. Int J Clin Oral Maxillofac Surg. 2018;4(1):4-10. doi: 10.11648/j.ijcoms.20180401.12

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  • @article{10.11648/j.ijcoms.20180401.12,
      author = {Cárcamo Idiáquez Osmar Adán and Cortes Flores Michelle and Anchecta Castro Diana Marielos and Vivanco Pérez Israel and Navarro Zarate Adolfo},
      title = {Fibrodysplasia Ossificans Progressiva: A Review with Presentation of a Case with Temporomandibular Extra-Articular Ankylosis},
      journal = {International Journal of Clinical Oral and Maxillofacial Surgery},
      volume = {4},
      number = {1},
      pages = {4-10},
      doi = {10.11648/j.ijcoms.20180401.12},
      url = {https://doi.org/10.11648/j.ijcoms.20180401.12},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcoms.20180401.12},
      abstract = {Fibrodysplasia Ossificans Progressiva (FOP) is a connective tissue disorder that progressively affects tendons, ligaments, aponeurosis, fasciae and muscles which undergo fibrous cell proliferation that progresses to mature bone. It has a prevalence of 1 case per 2 million habitants, having reported less than 1000 cases worldwide. In the maxillofacial region, it might originate extra-articular temporomandibular ankylosis by ossification of ligaments, muscles of the mastication, head and a neck muscles; the most commonly affected are the masseters and sternocleidomastoids. The purpose of this article is to review the Fibrodysplasia Ossificans Progressiva (FOP) and to present the case of a 12-year-old male patient with FOP that causes extra-articular temporomandibular ankylosis. There is no effective proven treatment or prevention and the life expectancy of these patients approaches the 40 years of age, so the management of patients with FOP must be performed with a multidisciplinary approach in which the various health professionals work in a coordinated and joint way to offer a better quality of life to these patients and thus better understand the progression of the disease.},
     year = {2018}
    }
    

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    AB  - Fibrodysplasia Ossificans Progressiva (FOP) is a connective tissue disorder that progressively affects tendons, ligaments, aponeurosis, fasciae and muscles which undergo fibrous cell proliferation that progresses to mature bone. It has a prevalence of 1 case per 2 million habitants, having reported less than 1000 cases worldwide. In the maxillofacial region, it might originate extra-articular temporomandibular ankylosis by ossification of ligaments, muscles of the mastication, head and a neck muscles; the most commonly affected are the masseters and sternocleidomastoids. The purpose of this article is to review the Fibrodysplasia Ossificans Progressiva (FOP) and to present the case of a 12-year-old male patient with FOP that causes extra-articular temporomandibular ankylosis. There is no effective proven treatment or prevention and the life expectancy of these patients approaches the 40 years of age, so the management of patients with FOP must be performed with a multidisciplinary approach in which the various health professionals work in a coordinated and joint way to offer a better quality of life to these patients and thus better understand the progression of the disease.
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Author Information
  • Maxillofacial Surgery Department, Meritorious Autonomous University of Puebla, Puebla, Mexico

  • Maxillofacial Surgery Department, Mexican Institute of Social Security, Guadalajara, Mexico

  • Faculty of Stomatology, Meritorious Autonomous University of Puebla, Puebla, Mexico

  • Maxillofacial Surgery Department, Meritorious Autonomous University of Puebla, Puebla, Mexico

  • Maxillofacial Surgery Department, Meritorious Autonomous University of Puebla, Puebla, Mexico

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