Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia

Hicham Bakkali; Salahedine Massou; Fayçal Labrini; Khalil Mounir; Mustapha Bensghir; Hicham Azendour; Hicham Balkhi; Charqui Haimeur

doi:doi:10.11648/j.ja.20130103.12

Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia

Hicham Bakkali, Salahedine Massou, Fayçal Labrini, Khalil Mounir, Mustapha Bensghir, Hicham Azendour, Hicham Balkhi, Charqui Haimeur

Published in Journal of Anesthesiology (Volume 1, Issue 3)

Received: 27 October 2013 Accepted: Published: 20 November 2013

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Abstract

The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII.

Published in	Journal of Anesthesiology (Volume 1, Issue 3)
DOI	10.11648/j.ja.20130103.12
Page(s)	24-26
Creative Commons	This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.
Copyright	Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Anesthesia, Coagulation, Congenital Deficiency, Factor VII, Hemorrhage

References

[1]	Meaudre E, Kenane N, Kaiser E, Gaillard PE, Saillol A, Cantais E, Palmier B. Isolated acquired factor VII deficiency in patient with severe head trauma: use of factor VII (factor VII-LFB). Ann Fr Anesth Reanim 2005;24:1383–6.
[2]	Ragni MV, Lewis JH, Spero JA, Hasiba U. Factor VII deficiency. Am J Hematol 1981; 10: 79-88.
[3]	Perry DJ. Factor VII deficiency. Br J haematol 2002;118 (3):689-700.
[4]	Doran SE, Henry TR, Bockenstedt PL, Ross DA. Uncomplicated stereotactic and open surgical procedures in patients with factor VII deficiency. Surg Neurol 1994 ; 42 : 79 – 82.
[5]	Mathilde HB, Guillin MC, Kenneth AB. Les déficits constitutionnels en facteur VII de la coagulation et les mécanismes moléculaires qui en sont responsables. Hématologie 1999; 5: 199-205.
[6]	Park HK, Horowitz M, Jungreis C, Genevro J, Koebbe C, Levy E, Kassam E. Periprocedural morbidity and mortality associated with endovascular treatment of intracranial anevrysms. AJNR Am J Neuroradiol 2005; 26: 506–14.
[7]	Norback O, Gal G, Johansson M, Solander S, Tovi M, Persson L, Ronne-Engström E, Enblad P. The establishment of endovascular aneurysm coiling at a neurovascular unit: report of experience during early years. Neuroradiology 2005; 47: 144–52.
[8]	Ranchère JY, Ménart C, Lienhart A, Attali O. Factor VII deficiency and surgery. Ann Fr Anesth Réanim 1999; 18 :772-775.
[9]	Roberts HR, Monroe DM, Escobar MA. Current concepts of hemostasis: implications for therapy. Anesthesiology 2004; 100:722– 30.
[10]	Saint-Raymond S, Greffe B, Carré J, Pujante C, Goguel A . Practical approaches for surgical procedures in congenital factor VII deficiency. Ann Fr Anesth Réanim.1989, 8 :518-521.
[11]	Muleo G, Santaro R, Iannacaro PG, Papaleo P, Leo F. The use of recombinant activated factor VII in congenital and acquired factor VII deficiency. Blood Coag Fibrinolysis 1998; 9: 389-90.
[12]	Bolton-Maggs PH, Perry DJ, Chalmers EA, Parapia LA, Wilde JT, Williams MD, Collins PW, Kitchen S, Dolan G, Mumford AD. The rare coagulation disorders--review with guidelines for management from the United Kingdom Haemophilia Centre Doctors' Organisation. Haemophilia 2004; 10:593–628.

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APA Style

Hicham Bakkali, Salahedine Massou, Fayçal Labrini, Khalil Mounir, Mustapha Bensghir, et al. (2013). Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. International Journal of Anesthesia and Clinical Medicine, 1(3), 24-26. https://doi.org/10.11648/j.ja.20130103.12

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ACS Style

Hicham Bakkali; Salahedine Massou; Fayçal Labrini; Khalil Mounir; Mustapha Bensghir, et al. Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. Int. J. Anesth. Clin. Med. 2013, 1(3), 24-26. doi: 10.11648/j.ja.20130103.12

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AMA Style

Hicham Bakkali, Salahedine Massou, Fayçal Labrini, Khalil Mounir, Mustapha Bensghir, et al. Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. Int J Anesth Clin Med. 2013;1(3):24-26. doi: 10.11648/j.ja.20130103.12

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@article{10.11648/j.ja.20130103.12,
  author = {Hicham Bakkali and Salahedine Massou and Fayçal Labrini and Khalil Mounir and Mustapha Bensghir and Hicham Azendour and Hicham Balkhi and Charqui Haimeur},
  title = {Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia},
  journal = {International Journal of Anesthesia and Clinical Medicine},
  volume = {1},
  number = {3},
  pages = {24-26},
  doi = {10.11648/j.ja.20130103.12},
  url = {https://doi.org/10.11648/j.ja.20130103.12},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ja.20130103.12},
  abstract = {The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII.},
 year = {2013}
}

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TY  - JOUR
T1  - Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia
AU  - Hicham Bakkali
AU  - Salahedine Massou
AU  - Fayçal Labrini
AU  - Khalil Mounir
AU  - Mustapha Bensghir
AU  - Hicham Azendour
AU  - Hicham Balkhi
AU  - Charqui Haimeur
Y1  - 2013/11/20
PY  - 2013
N1  - https://doi.org/10.11648/j.ja.20130103.12
DO  - 10.11648/j.ja.20130103.12
T2  - International Journal of Anesthesia and Clinical Medicine
JF  - International Journal of Anesthesia and Clinical Medicine
JO  - International Journal of Anesthesia and Clinical Medicine
SP  - 24
EP  - 26
PB  - Science Publishing Group
SN  - 2997-2698
UR  - https://doi.org/10.11648/j.ja.20130103.12
AB  - The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII.
VL  - 1
IS  - 3
ER  -

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Author Information

Hicham Bakkali

Department of Anesthesiology and Critical Care, Military Training Hospital Med V, Rabat, Morocco
Salahedine Massou

Department of Anesthesiology and Critical Care, Military Training Hospital Med V, Rabat, Morocco
Fayçal Labrini
Khalil Mounir

Department of Anesthesiology and Critical Care, Military Training Hospital Med V, Rabat, Morocco
Mustapha Bensghir

Department of Anesthesiology and Critical Care, Military Training Hospital Med V, Rabat, Morocco
Hicham Azendour

Department of Anesthesiology and Critical Care, Military Training Hospital Med V, Rabat, Morocco
Hicham Balkhi

Department of Anesthesiology and Critical Care, Military Training Hospital Med V, Rabat, Morocco
Charqui Haimeur

Department of Anesthesiology and Critical Care, Military Training Hospital Med V, Rabat, Morocco

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APA Style

Hicham Bakkali, Salahedine Massou, Fayçal Labrini, Khalil Mounir, Mustapha Bensghir, et al. (2013). Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. International Journal of Anesthesia and Clinical Medicine, 1(3), 24-26. https://doi.org/10.11648/j.ja.20130103.12

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ACS Style

Hicham Bakkali; Salahedine Massou; Fayçal Labrini; Khalil Mounir; Mustapha Bensghir, et al. Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. Int. J. Anesth. Clin. Med. 2013, 1(3), 24-26. doi: 10.11648/j.ja.20130103.12

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AMA Style

Hicham Bakkali, Salahedine Massou, Fayçal Labrini, Khalil Mounir, Mustapha Bensghir, et al. Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia. Int J Anesth Clin Med. 2013;1(3):24-26. doi: 10.11648/j.ja.20130103.12

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@article{10.11648/j.ja.20130103.12,
  author = {Hicham Bakkali and Salahedine Massou and Fayçal Labrini and Khalil Mounir and Mustapha Bensghir and Hicham Azendour and Hicham Balkhi and Charqui Haimeur},
  title = {Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia},
  journal = {International Journal of Anesthesia and Clinical Medicine},
  volume = {1},
  number = {3},
  pages = {24-26},
  doi = {10.11648/j.ja.20130103.12},
  url = {https://doi.org/10.11648/j.ja.20130103.12},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ja.20130103.12},
  abstract = {The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII.},
 year = {2013}
}

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TY  - JOUR
T1  - Congenital Deficiency in Factor VII of the Coagulation and the Anesthesia
AU  - Hicham Bakkali
AU  - Salahedine Massou
AU  - Fayçal Labrini
AU  - Khalil Mounir
AU  - Mustapha Bensghir
AU  - Hicham Azendour
AU  - Hicham Balkhi
AU  - Charqui Haimeur
Y1  - 2013/11/20
PY  - 2013
N1  - https://doi.org/10.11648/j.ja.20130103.12
DO  - 10.11648/j.ja.20130103.12
T2  - International Journal of Anesthesia and Clinical Medicine
JF  - International Journal of Anesthesia and Clinical Medicine
JO  - International Journal of Anesthesia and Clinical Medicine
SP  - 24
EP  - 26
PB  - Science Publishing Group
SN  - 2997-2698
UR  - https://doi.org/10.11648/j.ja.20130103.12
AB  - The constitutional deficiency in factor VII (FVII) of the coagulation is a rare autosomal recessive disease, responsible for a hemorrhagic syndrome of variable intensity poorly correlated with plasma levels of FVII. This deficit is suspected in front of an isolated reduction in the rate of prothrombine and confirmed by the dosage of this factor. We report a case of congenital FVII deficiency in a patient aged 22 years, who underwent surgical treatment of nephrolithiasis. FVII deficiency was 22%, no replacement therapy was introduced to the patient, and no bleeding complications were observed in intraoperative or postoperative. In conclusion, the perioperative transfusion with fresh frozen plasma (FFP) or the contribution of FVII in a patient with a moderate deficit in FVII is not systematic, and it cannot be considered if there is a risk of bleeding or in case of deficiency of FVII.
VL  - 1
IS  - 3
ER  -

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