Background: Progressive familiar intrahepatic cholestasis (PFIC) is a group of rare cholestatic liver diseases whose main features are itching, jaundice and even liver failure. Many studies have been reported in clinical reports, but the care of PFIC is rarely described. Purpose: To provide a summary and recommendations for the setup of strategies for PFIC patient care. Material and methods: A non-systematic review of PFIC nursing research until July 12, 2020. Use online search engines (PubMed, Medline, Embase, Web of Science, and CINAHL) to find PFIC nursing-related content, sort and summarize nursing-related content. Results: As a rare disease, there is limited research in PFIC nursing. The main care measures of PFIC including nursing interventions and evaluation tools. Nursing intervention is divided into general symptom care and nursing care of postoperative complications. Evaluation tools mainly focus on quality of life assessment and evaluation of itching. Conclusions: Nurses should pay attention to the use of scales when caring for PFIC patients, and observe whether specific nursing measures can help improve patients’ quality of life. PFIC nursing interventions and evaluation tools should be tailored according to PFIC clinical manifestation. A multidisciplinary collaborative approach is encouraged for proper management and tailoring therapy according to clinical manifestation.
| Published in | American Journal of Nursing Science (Volume 9, Issue 5) |
| DOI | 10.11648/j.ajns.20200905.11 |
| Page(s) | 310-315 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2024. Published by Science Publishing Group |
Progressive Familial Intrahepatic Cholestasis (PFIC), Nursing, Evaluation, Itching, Quality of Life, Intervention
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APA Style
Ni Zhang, Yuanzong Song, Meixue Chen, Lingli Cai, Manli Liu, et al. (2020). Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis. American Journal of Nursing Science, 9(5), 310-315. https://doi.org/10.11648/j.ajns.20200905.11
ACS Style
Ni Zhang; Yuanzong Song; Meixue Chen; Lingli Cai; Manli Liu, et al. Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis. Am. J. Nurs. Sci. 2020, 9(5), 310-315. doi: 10.11648/j.ajns.20200905.11
AMA Style
Ni Zhang, Yuanzong Song, Meixue Chen, Lingli Cai, Manli Liu, et al. Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis. Am J Nurs Sci. 2020;9(5):310-315. doi: 10.11648/j.ajns.20200905.11
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Download@article{10.11648/j.ajns.20200905.11,
author = {Ni Zhang and Yuanzong Song and Meixue Chen and Lingli Cai and Manli Liu and Weiwei Wang and Qingran Lin},
title = {Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis},
journal = {American Journal of Nursing Science},
volume = {9},
number = {5},
pages = {310-315},
doi = {10.11648/j.ajns.20200905.11},
url = {https://doi.org/10.11648/j.ajns.20200905.11},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajns.20200905.11},
abstract = {Background: Progressive familiar intrahepatic cholestasis (PFIC) is a group of rare cholestatic liver diseases whose main features are itching, jaundice and even liver failure. Many studies have been reported in clinical reports, but the care of PFIC is rarely described. Purpose: To provide a summary and recommendations for the setup of strategies for PFIC patient care. Material and methods: A non-systematic review of PFIC nursing research until July 12, 2020. Use online search engines (PubMed, Medline, Embase, Web of Science, and CINAHL) to find PFIC nursing-related content, sort and summarize nursing-related content. Results: As a rare disease, there is limited research in PFIC nursing. The main care measures of PFIC including nursing interventions and evaluation tools. Nursing intervention is divided into general symptom care and nursing care of postoperative complications. Evaluation tools mainly focus on quality of life assessment and evaluation of itching. Conclusions: Nurses should pay attention to the use of scales when caring for PFIC patients, and observe whether specific nursing measures can help improve patients’ quality of life. PFIC nursing interventions and evaluation tools should be tailored according to PFIC clinical manifestation. A multidisciplinary collaborative approach is encouraged for proper management and tailoring therapy according to clinical manifestation.},
year = {2020}
}
TY - JOUR T1 - Summary and Considerations in the Nursing Care of Patients with Progressive Familial Intrahepatic Cholestasis AU - Ni Zhang AU - Yuanzong Song AU - Meixue Chen AU - Lingli Cai AU - Manli Liu AU - Weiwei Wang AU - Qingran Lin Y1 - 2020/08/19 PY - 2020 N1 - https://doi.org/10.11648/j.ajns.20200905.11 DO - 10.11648/j.ajns.20200905.11 T2 - American Journal of Nursing Science JF - American Journal of Nursing Science JO - American Journal of Nursing Science SP - 310 EP - 315 PB - Science Publishing Group SN - 2328-5753 UR - https://doi.org/10.11648/j.ajns.20200905.11 AB - Background: Progressive familiar intrahepatic cholestasis (PFIC) is a group of rare cholestatic liver diseases whose main features are itching, jaundice and even liver failure. Many studies have been reported in clinical reports, but the care of PFIC is rarely described. Purpose: To provide a summary and recommendations for the setup of strategies for PFIC patient care. Material and methods: A non-systematic review of PFIC nursing research until July 12, 2020. Use online search engines (PubMed, Medline, Embase, Web of Science, and CINAHL) to find PFIC nursing-related content, sort and summarize nursing-related content. Results: As a rare disease, there is limited research in PFIC nursing. The main care measures of PFIC including nursing interventions and evaluation tools. Nursing intervention is divided into general symptom care and nursing care of postoperative complications. Evaluation tools mainly focus on quality of life assessment and evaluation of itching. Conclusions: Nurses should pay attention to the use of scales when caring for PFIC patients, and observe whether specific nursing measures can help improve patients’ quality of life. PFIC nursing interventions and evaluation tools should be tailored according to PFIC clinical manifestation. A multidisciplinary collaborative approach is encouraged for proper management and tailoring therapy according to clinical manifestation. VL - 9 IS - 5 ER -
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