Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case

Mbaye Diaw; Papa Alassane Leye; Alioune Badara Thiam; Abdou Kane Diop; El Hadj Ndiasse Diop; Ndeye Aissatou Bagayogo; Sagar Diop; Mouhamadou Moustapha Ndongo; Papa Ibrahima Ndiaye; Elisabeth Diouf

doi:doi:10.11648/j.ijacm.20221001.17

Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case

Mbaye Diaw, Papa Alassane Leye, Alioune Badara Thiam, Abdou Kane Diop, El Hadj Ndiasse Diop, Ndeye Aissatou Bagayogo, Sagar Diop, Mouhamadou Moustapha Ndongo, Papa Ibrahima Ndiaye, Elisabeth Diouf

Published in International Journal of Anesthesia and Clinical Medicine (Volume 10, Issue 1)

Received: 16 May 2022 Accepted: 14 June 2022 Published: 27 June 2022

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Abstract

The royal tumor is a very hemorrhagic tumor reflecting the preponderant and monstrous development of a plexiform neurofibroma or a deep tumor of a nerve trunk. We report the case of a 29-year-old patient with a large and painful tumor attached to the lumbosacral region by an implantation base 40cm wide, avoiding dorsal decubitus and associated with symptoms of slow dorsal spinal cord compression and diffuse cutaneous neurofibromas localized on the face, neck and thorax. MRI showed a large soft tissue tumor with intraspinal invasion in D8. Histology of the tumor confirmed the diagnosis of neurofibromatosis at the stage of cancerization with a profile in favor of a leiomyosarcoma with a myxoid aspect. We present through this case the possibility of the preponderant and monstrous development of a neurofibroma of Von Recklinghausen, his cancerization and the challenge of the anesthetic management.

Published in	International Journal of Anesthesia and Clinical Medicine (Volume 10, Issue 1)
DOI	10.11648/j.ijacm.20221001.17
Page(s)	38-43
Creative Commons	This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.
Copyright	Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Neurofibroma, Von Recklinghausen, Anesthesia, Dakar

References

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APA Style

Mbaye Diaw, Papa Alassane Leye, Alioune Badara Thiam, Abdou Kane Diop, El Hadj Ndiasse Diop, et al. (2022). Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case. International Journal of Anesthesia and Clinical Medicine, 10(1), 38-43. https://doi.org/10.11648/j.ijacm.20221001.17

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ACS Style

Mbaye Diaw; Papa Alassane Leye; Alioune Badara Thiam; Abdou Kane Diop; El Hadj Ndiasse Diop, et al. Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case. Int. J. Anesth. Clin. Med. 2022, 10(1), 38-43. doi: 10.11648/j.ijacm.20221001.17

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AMA Style

Mbaye Diaw, Papa Alassane Leye, Alioune Badara Thiam, Abdou Kane Diop, El Hadj Ndiasse Diop, et al. Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case. Int J Anesth Clin Med. 2022;10(1):38-43. doi: 10.11648/j.ijacm.20221001.17

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@article{10.11648/j.ijacm.20221001.17,
  author = {Mbaye Diaw and Papa Alassane Leye and Alioune Badara Thiam and Abdou Kane Diop and El Hadj Ndiasse Diop and Ndeye Aissatou Bagayogo and Sagar Diop and Mouhamadou Moustapha Ndongo and Papa Ibrahima Ndiaye and Elisabeth Diouf},
  title = {Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case},
  journal = {International Journal of Anesthesia and Clinical Medicine},
  volume = {10},
  number = {1},
  pages = {38-43},
  doi = {10.11648/j.ijacm.20221001.17},
  url = {https://doi.org/10.11648/j.ijacm.20221001.17},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijacm.20221001.17},
  abstract = {The royal tumor is a very hemorrhagic tumor reflecting the preponderant and monstrous development of a plexiform neurofibroma or a deep tumor of a nerve trunk. We report the case of a 29-year-old patient with a large and painful tumor attached to the lumbosacral region by an implantation base 40cm wide, avoiding dorsal decubitus and associated with symptoms of slow dorsal spinal cord compression and diffuse cutaneous neurofibromas localized on the face, neck and thorax. MRI showed a large soft tissue tumor with intraspinal invasion in D8. Histology of the tumor confirmed the diagnosis of neurofibromatosis at the stage of cancerization with a profile in favor of a leiomyosarcoma with a myxoid aspect. We present through this case the possibility of the preponderant and monstrous development of a neurofibroma of Von Recklinghausen, his cancerization and the challenge of the anesthetic management.},
 year = {2022}
}

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TY  - JOUR
T1  - Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case
AU  - Mbaye Diaw
AU  - Papa Alassane Leye
AU  - Alioune Badara Thiam
AU  - Abdou Kane Diop
AU  - El Hadj Ndiasse Diop
AU  - Ndeye Aissatou Bagayogo
AU  - Sagar Diop
AU  - Mouhamadou Moustapha Ndongo
AU  - Papa Ibrahima Ndiaye
AU  - Elisabeth Diouf
Y1  - 2022/06/27
PY  - 2022
N1  - https://doi.org/10.11648/j.ijacm.20221001.17
DO  - 10.11648/j.ijacm.20221001.17
T2  - International Journal of Anesthesia and Clinical Medicine
JF  - International Journal of Anesthesia and Clinical Medicine
JO  - International Journal of Anesthesia and Clinical Medicine
SP  - 38
EP  - 43
PB  - Science Publishing Group
SN  - 2997-2698
UR  - https://doi.org/10.11648/j.ijacm.20221001.17
AB  - The royal tumor is a very hemorrhagic tumor reflecting the preponderant and monstrous development of a plexiform neurofibroma or a deep tumor of a nerve trunk. We report the case of a 29-year-old patient with a large and painful tumor attached to the lumbosacral region by an implantation base 40cm wide, avoiding dorsal decubitus and associated with symptoms of slow dorsal spinal cord compression and diffuse cutaneous neurofibromas localized on the face, neck and thorax. MRI showed a large soft tissue tumor with intraspinal invasion in D8. Histology of the tumor confirmed the diagnosis of neurofibromatosis at the stage of cancerization with a profile in favor of a leiomyosarcoma with a myxoid aspect. We present through this case the possibility of the preponderant and monstrous development of a neurofibroma of Von Recklinghausen, his cancerization and the challenge of the anesthetic management.
VL  - 10
IS  - 1
ER  -

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Author Information

Mbaye Diaw

Anesthesia and Critical Care Medicine, Cheikh Anta Diop University (UCAD), Dakar, Senega
Papa Alassane Leye

Faculty of Medicine, Pharmacy and Odonto-Stomatology, Cheikh Anta Diop University (UCAD), Dakar, Senegal
Alioune Badara Thiam

Department of Neurosurgery, Fann University National Hospital, Dakar, Senegal
Abdou Kane Diop

Department of Anesthesia and Critical Care Medicine, Aristide Le Dantec University Hospital, Dakar, Senegal
El Hadj Ndiasse Diop

Faculty of Medicine, Pharmacy and Odonto-Stomatology, Cheikh Anta Diop University (UCAD), Dakar, Senegal
Ndeye Aissatou Bagayogo

Faculty of Medicine, Pharmacy and Odonto-Stomatology, Cheikh Anta Diop University (UCAD), Dakar, Senegal
Sagar Diop

Department of Neurosurgery, Fann University National Hospital, Dakar, Senegal
Mouhamadou Moustapha Ndongo

Department of Neurosurgery, Fann University National Hospital, Dakar, Senegal
Papa Ibrahima Ndiaye

Faculty of Medicine, Pharmacy and Odonto-Stomatology, Cheikh Anta Diop University (UCAD), Dakar, Senegal
Elisabeth Diouf

Faculty of Medicine, Pharmacy and Odonto-Stomatology, Cheikh Anta Diop University (UCAD), Dakar, Senegal

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APA Style

Mbaye Diaw, Papa Alassane Leye, Alioune Badara Thiam, Abdou Kane Diop, El Hadj Ndiasse Diop, et al. (2022). Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case. International Journal of Anesthesia and Clinical Medicine, 10(1), 38-43. https://doi.org/10.11648/j.ijacm.20221001.17

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ACS Style

Mbaye Diaw; Papa Alassane Leye; Alioune Badara Thiam; Abdou Kane Diop; El Hadj Ndiasse Diop, et al. Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case. Int. J. Anesth. Clin. Med. 2022, 10(1), 38-43. doi: 10.11648/j.ijacm.20221001.17

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AMA Style

Mbaye Diaw, Papa Alassane Leye, Alioune Badara Thiam, Abdou Kane Diop, El Hadj Ndiasse Diop, et al. Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case. Int J Anesth Clin Med. 2022;10(1):38-43. doi: 10.11648/j.ijacm.20221001.17

Copy | Download

@article{10.11648/j.ijacm.20221001.17,
  author = {Mbaye Diaw and Papa Alassane Leye and Alioune Badara Thiam and Abdou Kane Diop and El Hadj Ndiasse Diop and Ndeye Aissatou Bagayogo and Sagar Diop and Mouhamadou Moustapha Ndongo and Papa Ibrahima Ndiaye and Elisabeth Diouf},
  title = {Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case},
  journal = {International Journal of Anesthesia and Clinical Medicine},
  volume = {10},
  number = {1},
  pages = {38-43},
  doi = {10.11648/j.ijacm.20221001.17},
  url = {https://doi.org/10.11648/j.ijacm.20221001.17},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijacm.20221001.17},
  abstract = {The royal tumor is a very hemorrhagic tumor reflecting the preponderant and monstrous development of a plexiform neurofibroma or a deep tumor of a nerve trunk. We report the case of a 29-year-old patient with a large and painful tumor attached to the lumbosacral region by an implantation base 40cm wide, avoiding dorsal decubitus and associated with symptoms of slow dorsal spinal cord compression and diffuse cutaneous neurofibromas localized on the face, neck and thorax. MRI showed a large soft tissue tumor with intraspinal invasion in D8. Histology of the tumor confirmed the diagnosis of neurofibromatosis at the stage of cancerization with a profile in favor of a leiomyosarcoma with a myxoid aspect. We present through this case the possibility of the preponderant and monstrous development of a neurofibroma of Von Recklinghausen, his cancerization and the challenge of the anesthetic management.},
 year = {2022}
}

Copy | Download

TY  - JOUR
T1  - Peri-Operative Management of a Von Recklinghausen's Disease Royal Tumor: About a Case
AU  - Mbaye Diaw
AU  - Papa Alassane Leye
AU  - Alioune Badara Thiam
AU  - Abdou Kane Diop
AU  - El Hadj Ndiasse Diop
AU  - Ndeye Aissatou Bagayogo
AU  - Sagar Diop
AU  - Mouhamadou Moustapha Ndongo
AU  - Papa Ibrahima Ndiaye
AU  - Elisabeth Diouf
Y1  - 2022/06/27
PY  - 2022
N1  - https://doi.org/10.11648/j.ijacm.20221001.17
DO  - 10.11648/j.ijacm.20221001.17
T2  - International Journal of Anesthesia and Clinical Medicine
JF  - International Journal of Anesthesia and Clinical Medicine
JO  - International Journal of Anesthesia and Clinical Medicine
SP  - 38
EP  - 43
PB  - Science Publishing Group
SN  - 2997-2698
UR  - https://doi.org/10.11648/j.ijacm.20221001.17
AB  - The royal tumor is a very hemorrhagic tumor reflecting the preponderant and monstrous development of a plexiform neurofibroma or a deep tumor of a nerve trunk. We report the case of a 29-year-old patient with a large and painful tumor attached to the lumbosacral region by an implantation base 40cm wide, avoiding dorsal decubitus and associated with symptoms of slow dorsal spinal cord compression and diffuse cutaneous neurofibromas localized on the face, neck and thorax. MRI showed a large soft tissue tumor with intraspinal invasion in D8. Histology of the tumor confirmed the diagnosis of neurofibromatosis at the stage of cancerization with a profile in favor of a leiomyosarcoma with a myxoid aspect. We present through this case the possibility of the preponderant and monstrous development of a neurofibroma of Von Recklinghausen, his cancerization and the challenge of the anesthetic management.
VL  - 10
IS  - 1
ER  -

Copy | Download